symptom of the type of the male pseudohermaphrodism

symptom of the type of the male pseudohermaphrodism
It is the incomplete testis of single development that the male pseudohermaphrodism patient has Y to dye the internal genitals, there is external genitalia at various degrees that behaves womanlikely.
Divided into three kinds of types according to two sexes intensity of external genitalia:
1,Male external genitalia type Penis development is close to normally but has urethras to leave and split; Often have cryptorchidism or inguinal defect, there are uterus and oviduct not ripe in the bag. It has the second sex character that appearance presents the male size. The pathogenic factor is that the male foetus fails to inhibit the development that manages of kidney of China in the embryo one, and uterus and oviduct this type which form the hypoplasia are also called pair and hit kidney and in charge of retaining syndrome.
2,Women's external genitalia type It is womanlike to also call the complete testis, the chromosome core type is 46, XY has guilt pill, a ball of ketone of guilt is normal in biosynthesis, the density of ketone of testis presents the normal level in the blood
The testis can present epididymis and spermatic duct at the same time in abdominal cavity's big overcast lip or inguinal hernia bag, also the patient lacks; It has clitoris, overcast lip and false vagina that the external genitalia shape is totally like women, but there are not ovarian oviducts and uteruses. Its pathological change lies in an patient organ of embryo and organizes cells to totally lack the androgenic receptor and stick albumens, make it develop, become women external genitalia can develop, succeed normal the intersection of women and breast and the intersection of women and figure adolescence since the childhood not to secrete the intersection of urine and the intersection of reproduction and sinus and the intersection of external genitalia and original base. Tide that but there is no period to come.
3,Some women's phenotype of external genitalia It is like the loose clitoris to leave splitting with the penis scrotum type urethra that the penis is short and small; The scrotum is split as the big overcast lip, include the testis; Have false vaginas, the reproduction sinus deformity of the urine; There are not women's uterus and attachment testis ketone that formate the obstacle, the incompleteness testis is womanlike, Reifenstein the intersection of syndrome and false vagina will bright the intersection of scrotum and urethra lay, split syndrome and unsymmetry mixing the intersection of gonad and development bad disease whether the intersection of external genitalia and some woman display Type.
In addition there is a kind of male pseudohermaphrodism, although chromosome is 46, XY has no testis, have no ovary, the external genitalia is called, had no gonad disease for the women type. The onset mechanism may be to cause the development of a genitals of embryo to be totally inhibited some patients from having family's history because of gene mutation, it may be recessive hereditary disease of the autosome.
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